Thrombotic thrombocytopenic purpura
Også kjent som: TTP
Engelsk navn: Thrombotic thrombocytopenic purpura
Engelske synonym: Moschcowitz disease,TTP
An aggressive and life-threatening form of thrombotic microangiopathy (TMA) characterized by profound peripheral thrombocytopenia, microangiopathic hemolytic anemia (MAHA) and organ failure of variable severity and is comprised of a congenital (cTTP) and acquired, immune-mediated (iTTP) form.