Primary immunodeficiency with post-measles-mumps-rubella vaccine viral infection


Engelsk navn: Primary immunodeficiency with post-measles-mumps-rubella vaccine viral infection
Engelske synonym: Primary immunodeficiency with post-MMR vaccine viral infection


Definisjon

Primary immunodeficiency with post-measles-mumps-rubella vaccine viral infection is a rare primary immunodeficiency due to a defect in innate immunity disorder characterized by selective susceptibility to viral infections, particularly after systemic challenge with live viral vaccines, such as the measles, mumps and rubella (MMR) vaccine. Patients present severe, potentially fatal, manifestations to viral illness, including encephalitis, hepatitis and pneumonitis.

Fra Orphanet

ORPHA: 431166
Klassifiseringsnivå: Disorder
ICD-10: D84.8

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