POEMS syndrom


Engelsk navn: POEMS syndrome
Engelske synonym: Crow-Fukase syndrome,Osteosclerotic myeloma,PEP syndrome,Polyneuropathy-endocrinopathy-plasma cell dyscrasia syndrome,Takatsuki syndrome


Definisjon

POEMS syndrome is a paraneoplastic syndrome characterized by polyradiculoneuropathy (P), organomegaly (O), endocrinopathy (E), clonal plasma cell disorder (M), and skin changes (S). Other features include papilledema, extravascular volume overload, sclerotic bone lesions, thrombocytosis/erythrocytosis, and elevated VEGF levels.

Fra Orphanet

ORPHA: 2905
Klassifiseringsnivå: Disorder
ICD-10: D47.7

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