Keratolytisk vinter-erytem
Engelsk navn: Keratolytic winter erythema
Engelske synonym: Erythrokeratolysis hiemalis,Oudtshoorn disease
Definisjon
Keratolytic winter erythema is a rare epidermal disease, characterized by recurrent centrifugal palmoplantar peeling and erythema presenting seasonal variation (cold weather). Skin lesions may spread to the dorsum of hands and feet and to the interdigital spaces. Lower legs, knees and thighs may also be involved. Episodes may be preceded by itch and hyperhidrosis. Skin biopsy reveals an epidermal spongiosis with clefting in the stratum corneum, followed by regrowth. Keratolytic winter erythema follows an autosomal dominant mode of transmission.
Fra Orphanet
ORPHA: 50943
Klassifiseringsnivå: Disorder
ICD-10: L30.8
Mer informasjon
Deler av informasjonen over er hentet fra ORPHAdata med lisens: Commons Attribution 4.0 International (CC BY 4.0)
