Juvenil dermatomyositt
Engelsk navn: Juvenile dermatomyositis
Engelske synonym: Juvenile DM
Definisjon
An early-onset form of dermatomyositis (DM), a systemic, autoimmune inflammatory muscle disorder with vasculopathy, characterized by proximal and symmetrical muscle weakness, evocative skin lesions, and systemic manifestations. Vasculopathy occurs in the skin, muscle (mainly in the perifascicular area), and sometimes in the intestinal tissue.
Fra Orphanet
ORPHA: 93672
Klassifiseringsnivå: Disorder
ICD-10: M33.0
Mer informasjon
Deler av informasjonen over er hentet fra ORPHAdata med lisens: Commons Attribution 4.0 International (CC BY 4.0)
