Juvenil dermatomyositt


Engelsk navn: Juvenile dermatomyositis
Engelske synonym: Juvenile DM


An early-onset form of dermatomyositis (DM), a systemic, autoimmune inflammatory muscle disorder with vasculopathy, characterized by proximal and symmetrical muscle weakness, evocative skin lesions, and systemic manifestations. Vasculopathy occurs in the skin, muscle (mainly in the perifascicular area), and sometimes in the intestinal tissue.



Informasjon

Norsk nevromuskulært kompetansesamarbeid har kunnskap om diagnosen.

ORPHA: 93672
Klassifiseringsnivå: Disorder
ICD-10: M33.0



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