Hydroa vacciniforme
Engelsk navn: Hydroa vacciniforme
Definisjon
A rare photodermatosis characterized by the development of pruritic or painful vesicles in a photodistributed pattern in response to sunlight exposure. The lesions heal with permanent varioliform scarring. Ocular involvement, deformities of ears and nose, or contractures of the fingers may occasionally be observed. Systemic signs and symptoms are absent. The condition typically occurs in childhood and regresses spontaneously in adolescence or young adulthood.
Fra Orphanet
ORPHA: 330058
Klassifiseringsnivå: Disorder
ICD-10: L56.4
Mer informasjon
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