Autoimmunt lymfoproliferativt syndom
Også kjent som: ALPS
Engelsk navn: Autoimmune lymphoproliferative syndrome
Engelske synonym: ALPS,Canale-Smith syndrome
Definisjon
A rare, inherited disorder characterized by non-malignant lymphoproliferation, multilineage cytopenias, and a lifelong increased risk of Hodgkin's and non-Hodgkin's lymphoma.
Fra Orphanet
ORPHA: 3261
Klassifiseringsnivå: Disorder
ICD-10: D47.9