von Willebrands sykdom, type III
Engelsk navn: Von Willebrand disease type 3
Definisjon
A form of von Willebrand disease (VWD) characterized by a bleeding disorder associated with a total or near-total absence of Willebrand factor (VWF) in the plasma and cellular compartments, also leading to a profound deficiency of plasmatic factor VIII (FVIII). It is the most severe form of VWD.
Fra Orphanet
ORPHA: 166096
Klassifiseringsnivå: Subtype of disorder
ICD-10: D68.0
Mer informasjon
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