von Willebrands sykdom, type III
Engelsk navn: Von Willebrand disease type 3
A form of von Willebrand disease (VWD) characterized by a bleeding disorder associated with a total or near-total absence of Willebrand factor (VWF) in the plasma and cellular compartments, also leading to a profound deficiency of plasmatic factor VIII (FVIII). It is the most severe form of VWD.
Klassifiseringsnivå: Subtype of disorder