Diazoxide‑resistant diffuse hyperinsulinism


Engelsk navn: Diazoxide-resistant diffuse hyperinsulinism
Engelske synonym: Hyperinsulinemic hypoglycemia, diazoxide-resistant diffuse form


Definisjon

Diazoxide-resistant diffuse hyperinsulism (DRDH) is a form of Diazoxide resistant hyperinsulinism (see this term) characterized by recurrent episodes of profound hypoglycemia caused by an excessive/ uncontrolled insulin secretion (inappropriate for the level of glycemia) due to diffuse involvement of pancreas that is unresponsive to medical treatment with diazoxide, often necessitating near total/total pancreatectomy.

Fra Orphanet

ORPHA: 165988
Klassifiseringsnivå: Group of disorders
ICD-10:

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